4-Methylumbelliferyl 6-Sulfo-2-acetamido-2-deoxy-β-D-glucopyranoside Potassium Salt

• Catalog No.: M335000
• CAS Number: 210357-38-3
• M. F.: C18H20KNO11S
• M. W.: 497.5148
• Storage: Hygroscopic, -20°C Freezer, Under Inert Atmosphere

SYNONYMS

• IUPAC name: potassium [(2R,3S,4R,5R,6S)-5-acetamido-3,4-dihydroxy-6-[(4-methyl-2-oxo-2H-chromen-7-yl)oxy]oxan-2-yl]methyl sulfate
• IUPAC Traditional name: potassium [(2R,3S,4R,5R,6S)-5-acetamido-3,4-dihydroxy-6-[(4-methyl-2-oxochromen-7-yl)oxy]oxan-2-yl]methyl sulfate
• Synonyms: 7-[[2-(Acetylamino)-2-deoxy-6-O-sulfo-β-D-glucopyranosyl]oxy]-4-methyl-2H-1-benzopyran-2-one Monopotassium Salt; MUGS

DATABASE IDS

• CAS Number: 210357-38-3

PROPERTIES

• Apperance: White Solid
• Melting Point: 190-193°C (dec.)
• Solubility: Water
• Storage Condition: Hygroscopic, -20°C Freezer, Under Inert Atmosphere
• Storage Warning: Light Sensitive - Protect from Light; Store at -20°C

DETAILS

Description (English)

A fluorogenic substrate used for the diagnosis of GM2 gangliosidoses in leukocytes. Genetic defects in human b-hexosaminidase isozymes (Hex A & Hex B) result in various clinical and biochemical types of GM2 gangliosidosis. They include Tay Sachs disease,

REFERENCES

• Clinical Genetics, 26, 318 (1984)
• Bayleran, J., et al.: Clin. Chem. Acta 143, 73 (1984)